Sua seleção (0)
Detalhe da pesquisa
1.
Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.
Cochrane Database Syst Rev;
(7): CD007168, 2013 Jul 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-23852992
2.
Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele.
N Engl J Med;
381(19): 1809-1819, 2019 11 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-31697873
3.
Human neutrophil peptides mediate endothelial-monocyte interaction, foam cell formation, and platelet activation.
Arterioscler Thromb Vasc Biol;
31(9): 2070-9, 2011 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-21817096
4.
VX-445-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.
N Engl J Med;
379(17): 1612-1620, 2018 10 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-30334692
5.
VX-659-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.
N Engl J Med;
379(17): 1599-1611, 2018 10 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-30334693
6.
Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial.
Lancet;
394(10212): 1940-1948, 2019 Nov 23.
Artigo
em Inglês
| MEDLINE | ID: mdl-31679946
7.
Tezacaftor-Ivacaftor in Residual-Function Heterozygotes with Cystic Fibrosis.
N Engl J Med;
377(21): 2024-2035, 2017 11 23.
Artigo
em Inglês
| MEDLINE | ID: mdl-29099333
8.
Burkholderia cenocepacia ET12 transmission in adults with cystic fibrosis.
Thorax;
2019 Nov 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-31732688
9.
First clinical trials of novel ENaC targeting therapy, SPX-101, in healthy volunteers and adults with cystic fibrosis.
Pulm Pharmacol Ther;
58: 101819, 2019 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-31302339
10.
Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.
Cochrane Database Syst Rev;
(1): CD007168, 2009 Jan 21.
Artigo
em Inglês
| MEDLINE | ID: mdl-19160327
11.
Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR.
Am J Respir Crit Care Med;
197(2): 214-224, 2018 01 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-28930490
12.
Differential signaling mechanisms of HNP-induced IL-8 production in human lung epithelial cells and monocytes.
J Cell Physiol;
214(3): 820-7, 2008 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-17786963
13.
Cystic fibrosis gene modifier SLC26A9 modulates airway response to CFTR-directed therapeutics.
Hum Mol Genet;
25(20): 4590-4600, 2016 10 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-28171547
14.
Effect of pulmonary exacerbations treated with oral antibiotics on clinical outcomes in cystic fibrosis.
Thorax;
72(4): 327-332, 2017 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-27539619
15.
Functional integrity in children with anoxic brain injury from drowning.
Hum Brain Mapp;
38(10): 4813-4831, 2017 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-28759710
16.
Activity of Tobramycin against Cystic Fibrosis Isolates of Burkholderia cepacia Complex Grown as Biofilms.
Antimicrob Agents Chemother;
60(1): 348-55, 2016 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-26503664
17.
In vitro efficacy of high-dose tobramycin against Burkholderia cepacia complex and Stenotrophomonas maltophilia isolates from cystic fibrosis patients.
Antimicrob Agents Chemother;
59(1): 711-3, 2015 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-25348526
18.
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation.
N Engl J Med;
365(18): 1663-72, 2011 Nov 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-22047557
19.
Does extensive genotyping and nasal potential difference testing clarify the diagnosis of cystic fibrosis among patients with single-organ manifestations of cystic fibrosis?
Thorax;
69(3): 254-60, 2014 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-24149827
20.
Long-term effect of CFTR modulator therapy on airway nitric oxide.
Eur Respir J;
2019 Oct 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-31601715