Pesquisa | Biblioteca Virtual em Saúde

1.

Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.

Tam, Julian; Nash, Edward F; Ratjen, Felix; Tullis, Elizabeth; Stephenson, Anne.

Cochrane Database Syst Rev; (7): CD007168, 2013 Jul 12.

Artigo em Inglês | MEDLINE | ID: mdl-23852992

2.

Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele.

Middleton, Peter G; Mall, Marcus A; Drevínek, Pavel; Lands, Larry C; McKone, Edward F; Polineni, Deepika; Ramsey, Bonnie W; Taylor-Cousar, Jennifer L; Tullis, Elizabeth; Vermeulen, François; Marigowda, Gautham; McKee, Charlotte M; Moskowitz, Samuel M; Nair, Nitin; Savage, Jessica; Simard, Christopher; Tian, Simon; Waltz, David; Xuan, Fengjuan; Rowe, Steven M; Jain, Raksha.

N Engl J Med; 381(19): 1809-1819, 2019 11 07.

Artigo em Inglês | MEDLINE | ID: mdl-31697873

3.

Human neutrophil peptides mediate endothelial-monocyte interaction, foam cell formation, and platelet activation.

Quinn, Kieran L; Henriques, Melanie; Tabuchi, Arata; Han, Bing; Yang, Hong; Cheng, Wei-Erh; Tole, Soumitra; Yu, Hanpo; Luo, Alice; Charbonney, Emmanuel; Tullis, Elizabeth; Lazarus, Alan; Robinson, Lisa A; Ni, Heyu; Peterson, Blake R; Kuebler, Wolfgang M; Slutsky, Arthur S; Zhang, Haibo.

Arterioscler Thromb Vasc Biol; 31(9): 2070-9, 2011 Sep.

Artigo em Inglês | MEDLINE | ID: mdl-21817096

4.

VX-445-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

Keating, Dominic; Marigowda, Gautham; Burr, Lucy; Daines, Cori; Mall, Marcus A; McKone, Edward F; Ramsey, Bonnie W; Rowe, Steven M; Sass, Laura A; Tullis, Elizabeth; McKee, Charlotte M; Moskowitz, Samuel M; Robertson, Sarah; Savage, Jessica; Simard, Christopher; Van Goor, Fredrick; Waltz, David; Xuan, Fengjuan; Young, Tim; Taylor-Cousar, Jennifer L.

N Engl J Med; 379(17): 1612-1620, 2018 10 25.

Artigo em Inglês | MEDLINE | ID: mdl-30334692

5.

VX-659-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

Davies, Jane C; Moskowitz, Samuel M; Brown, Cynthia; Horsley, Alexander; Mall, Marcus A; McKone, Edward F; Plant, Barry J; Prais, Dario; Ramsey, Bonnie W; Taylor-Cousar, Jennifer L; Tullis, Elizabeth; Uluer, Ahmet; McKee, Charlotte M; Robertson, Sarah; Shilling, Rebecca A; Simard, Christopher; Van Goor, Fredrick; Waltz, David; Xuan, Fengjuan; Young, Tim; Rowe, Steven M.

N Engl J Med; 379(17): 1599-1611, 2018 10 25.

Artigo em Inglês | MEDLINE | ID: mdl-30334693

6.

Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial.

Heijerman, Harry G M; McKone, Edward F; Downey, Damian G; Van Braeckel, Eva; Rowe, Steven M; Tullis, Elizabeth; Mall, Marcus A; Welter, John J; Ramsey, Bonnie W; McKee, Charlotte M; Marigowda, Gautham; Moskowitz, Samuel M; Waltz, David; Sosnay, Patrick R; Simard, Christopher; Ahluwalia, Neil; Xuan, Fengjuan; Zhang, Yaohua; Taylor-Cousar, Jennifer L; McCoy, Karen S.

Lancet; 394(10212): 1940-1948, 2019 Nov 23.

Artigo em Inglês | MEDLINE | ID: mdl-31679946

7.

Tezacaftor-Ivacaftor in Residual-Function Heterozygotes with Cystic Fibrosis.

Rowe, Steven M; Daines, Cori; Ringshausen, Felix C; Kerem, Eitan; Wilson, John; Tullis, Elizabeth; Nair, Nitin; Simard, Christopher; Han, Linda; Ingenito, Edward P; McKee, Charlotte; Lekstrom-Himes, Julie; Davies, Jane C.

N Engl J Med; 377(21): 2024-2035, 2017 11 23.

Artigo em Inglês | MEDLINE | ID: mdl-29099333

8.

Burkholderia cenocepacia ET12 transmission in adults with cystic fibrosis.

Blanchard, Ana C; Tang, Lin; Tadros, Manal; Muller, Matthew; Spilker, Theodore; Waters, Valerie J; LiPuma, John J; Tullis, Elizabeth.

Thorax; 2019 Nov 15.

Artigo em Inglês | MEDLINE | ID: mdl-31732688

9.

First clinical trials of novel ENaC targeting therapy, SPX-101, in healthy volunteers and adults with cystic fibrosis.

Couroux, Peter; Farias, Paulina; Rizvi, Leena; Griffin, Katherine; Hudson, Christie; Crowder, Timothy; Tarran, Robert; Tullis, Elizabeth.

Pulm Pharmacol Ther; 58: 101819, 2019 Oct.

Artigo em Inglês | MEDLINE | ID: mdl-31302339

10.

Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.

Nash, Edward F; Stephenson, Anne; Ratjen, Felix; Tullis, Elizabeth.

Cochrane Database Syst Rev; (1): CD007168, 2009 Jan 21.

Artigo em Inglês | MEDLINE | ID: mdl-19160327

11.

Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR.

Donaldson, Scott H; Pilewski, Joseph M; Griese, Matthias; Cooke, Jon; Viswanathan, Lakshmi; Tullis, Elizabeth; Davies, Jane C; Lekstrom-Himes, Julie A; Wang, Linda T.

Am J Respir Crit Care Med; 197(2): 214-224, 2018 01 15.

Artigo em Inglês | MEDLINE | ID: mdl-28930490

12.

Differential signaling mechanisms of HNP-induced IL-8 production in human lung epithelial cells and monocytes.

Syeda, Farisa; Liu, Hui-Yu; Tullis, Elizabeth; Liu, Mingyao; Slutsky, Arthur S; Zhang, Haibo.

J Cell Physiol; 214(3): 820-7, 2008 Mar.

Artigo em Inglês | MEDLINE | ID: mdl-17786963

13.

Cystic fibrosis gene modifier SLC26A9 modulates airway response to CFTR-directed therapeutics.

Strug, Lisa J; Gonska, Tanja; He, Gengming; Keenan, Katherine; Ip, Wan; Boëlle, Pierre-Yves; Lin, Fan; Panjwani, Naim; Gong, Jiafen; Li, Weili; Soave, David; Xiao, Bowei; Tullis, Elizabeth; Rabin, Harvey; Parkins, Michael D; Price, April; Zuberbuhler, Peter C; Corvol, Harriet; Ratjen, Felix; Sun, Lei; Bear, Christine E; Rommens, Johanna M.

Hum Mol Genet; 25(20): 4590-4600, 2016 10 15.

Artigo em Inglês | MEDLINE | ID: mdl-28171547

14.

Effect of pulmonary exacerbations treated with oral antibiotics on clinical outcomes in cystic fibrosis.

Stanojevic, Sanja; McDonald, Alexandra; Waters, Valerie; MacDonald, Sarah; Horton, Eric; Tullis, Elizabeth; Ratjen, Felix.

Thorax; 72(4): 327-332, 2017 04.

Artigo em Inglês | MEDLINE | ID: mdl-27539619

15.

Functional integrity in children with anoxic brain injury from drowning.

Ishaque, Mariam; Manning, Janessa H; Woolsey, Mary D; Franklin, Crystal G; Tullis, Elizabeth W; Beckmann, Christian F; Fox, Peter T.

Hum Brain Mapp; 38(10): 4813-4831, 2017 10.

Artigo em Inglês | MEDLINE | ID: mdl-28759710

16.

Activity of Tobramycin against Cystic Fibrosis Isolates of Burkholderia cepacia Complex Grown as Biofilms.

Kennedy, Sarah; Beaudoin, Trevor; Yau, Yvonne C W; Caraher, Emma; Zlosnik, James E A; Speert, David P; LiPuma, John J; Tullis, Elizabeth; Waters, Valerie.

Antimicrob Agents Chemother; 60(1): 348-55, 2016 01.

Artigo em Inglês | MEDLINE | ID: mdl-26503664

17.

In vitro efficacy of high-dose tobramycin against Burkholderia cepacia complex and Stenotrophomonas maltophilia isolates from cystic fibrosis patients.

Ratjen, Anina; Yau, Yvonne; Wettlaufer, Jillian; Matukas, Larissa; Zlosnik, James E A; Speert, David P; LiPuma, John J; Tullis, Elizabeth; Waters, Valerie.

Antimicrob Agents Chemother; 59(1): 711-3, 2015 Jan.

Artigo em Inglês | MEDLINE | ID: mdl-25348526

18.

A CFTR potentiator in patients with cystic fibrosis and the G551D mutation.

Ramsey, Bonnie W; Davies, Jane; McElvaney, N Gerard; Tullis, Elizabeth; Bell, Scott C; Drevínek, Pavel; Griese, Matthias; McKone, Edward F; Wainwright, Claire E; Konstan, Michael W; Moss, Richard; Ratjen, Felix; Sermet-Gaudelus, Isabelle; Rowe, Steven M; Dong, Qunming; Rodriguez, Sally; Yen, Karl; Ordoñez, Claudia; Elborn, J Stuart.

N Engl J Med; 365(18): 1663-72, 2011 Nov 03.

Artigo em Inglês | MEDLINE | ID: mdl-22047557

19.

Does extensive genotyping and nasal potential difference testing clarify the diagnosis of cystic fibrosis among patients with single-organ manifestations of cystic fibrosis?

Ooi, Chee Y; Dupuis, Annie; Ellis, Lynda; Jarvi, Keith; Martin, Sheelagh; Ray, Peter N; Steele, Leslie; Kortan, Paul; Gonska, Tanja; Dorfman, Ruslan; Solomon, Melinda; Zielenski, Julian; Corey, Mary; Tullis, Elizabeth; Durie, Peter.

Thorax; 69(3): 254-60, 2014 Mar.

Artigo em Inglês | MEDLINE | ID: mdl-24149827

20.

Long-term effect of CFTR modulator therapy on airway nitric oxide.

Grasemann, Hartmut; Klingel, Michelle; Avolio, Julie; Prentice, Carley; Gonska, Tanja; Tullis, Elizabeth; Ratjen, Felix.

Eur Respir J; 2019 Oct 10.

Artigo em Inglês | MEDLINE | ID: mdl-31601715

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Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.

Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele.

Human neutrophil peptides mediate endothelial-monocyte interaction, foam cell formation, and platelet activation.

VX-445-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

VX-659-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial.

Tezacaftor-Ivacaftor in Residual-Function Heterozygotes with Cystic Fibrosis.

Burkholderia cenocepacia ET12 transmission in adults with cystic fibrosis.

First clinical trials of novel ENaC targeting therapy, SPX-101, in healthy volunteers and adults with cystic fibrosis.

Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.

Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR.

Differential signaling mechanisms of HNP-induced IL-8 production in human lung epithelial cells and monocytes.

Cystic fibrosis gene modifier SLC26A9 modulates airway response to CFTR-directed therapeutics.

Effect of pulmonary exacerbations treated with oral antibiotics on clinical outcomes in cystic fibrosis.

Functional integrity in children with anoxic brain injury from drowning.

Activity of Tobramycin against Cystic Fibrosis Isolates of Burkholderia cepacia Complex Grown as Biofilms.

In vitro efficacy of high-dose tobramycin against Burkholderia cepacia complex and Stenotrophomonas maltophilia isolates from cystic fibrosis patients.

A CFTR potentiator in patients with cystic fibrosis and the G551D mutation.

Does extensive genotyping and nasal potential difference testing clarify the diagnosis of cystic fibrosis among patients with single-organ manifestations of cystic fibrosis?

Long-term effect of CFTR modulator therapy on airway nitric oxide.